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NGHIÊN CỨU LÂM SÀNG Issue: Số 114

Treatment outcomes of patients with Klippel-Trenaunay syndrome at the Vietnam National Heart Institute, Bach Mai Hospital

Lê Anh Tuấn: Viện Tim mạch Việt Nam, Bệnh viện Bạch Mai; Doãn Hữu Linh: Viện Tim mạch Việt Nam, Bệnh viện Bạch Mai; Nguyễn Tuấn Hải: Trường Đại học Y Hà Nội; Lê Thị Mến: Trường Đại học Y Hà Nội; Nguyễn Ngọc Linh: Trường Đại học Y Hà Nội;
Published: May 30, 2025
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Abstract

Overview: Klippel-Trenaunay syndrome (KTS) is a rare congenital vascular disorder with numerous complications that affect the patient’s health, mental well-being, and quality of life. Due to the complex nature of the syndrome, treatment needs to be individualized and multidisciplinary to achieve optimal outcomes. Assessing the safety and effectiveness of treatment methods is essential to develop a standardized treatment protocol and improve the quality of life for KTS patients.

Objective: To evaluate the treatment outcomes of KTS at the Vietnam National Heart Institute, Bach Mai Hospital.

Method: A retrospective study collecting primary data from medical records of patients diagnosed with KTS treated at the Vietnam National Heart Institute, Bach Mai Hospital.

Results: Treatment of 29 KTS patients showed that 89.7% of patients were treated with appropriate compression stockings or bandages; 86.2% of patients were prescribed pharmacological treatments, including venous support medications and pain relievers; 24.1% of patients were advised to wear shoes with high soles to balance with the healthy limb; and 17.2% of patients underwent endovascular intervention at Bach Mai Hospital. Short-term treatment measures showed promising results.

Conclusion: KTS treatment requires a combination of various treatment methods, chosen based on the severity of damage, patient condition, and the experience of each medical center. Patients need regular and long-term follow-up at specialized vascular centers to ensure accurate diagnosis and treatment advice, avoiding missed complications.

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Section NGHIÊN CỨU LÂM SÀNG
Issue Số 114