Abstract
Introduction: Although perforation leaflet of Mitral valve aneurysms (MVAs) are rare, they usually occur commonly in the anterior leaflet mitral valve is associated with endocarditis of the aortic valve. Various mechanisms have been suggested for the etiopathogenesis of MVA. Case presentation: We present a case with perforated on the huge posterior leaflet mitral valve aneurysm due to infective endocarditis (IE) without significant regurgitation aortic valve, initially mistaken diagnosis of myxoma atria tumor, which was confirmed at transesophageal cardiogram. Conclusion: Perforated giant aneurysm of the posterior mitral leaflet valve is a rare but deadly complication of IE. It is mistaken to diagnose with TEE in the mitral valve aneurysm with vegetation and emphasize the role of TEE in early accurate diagnosis.